Pulmonary calcified masses and gastric tumor: Incomplete Carney's triad.

A 31-year-old woman presented with a 6-month history of dyspnea and posterior chest pain. Chest radiography demonstrated the presence of two round calcified pulmonary lesions. Results of physical examination and laboratory tests were normal. Chest computed tomography (CT) showed a well-circumscribed mass measuring 6 × 4 cm and a nodule with a diameter of 3 cm, both heavily calcified (Fig. 1A and B). Thoracostomy was performed with pulmonary segmentectomy and resection of both lesions. Microscopically, the tumors corresponded to a benign cartilaginous neoplasm, compatible with chondroma (Fig. 1C). Abdominal CT showed an exophytic gastric lesion (Fig. 1D). Laparoscopy with gastric biopsy demonstrated that this lesion was a gastrointestinal stromal tumor (GIST). Total gastrectomy was performed. The patient was discharged in good condition. No evidence of recurrence was detected at a 3-year follow-up examination. Carney triad is a rare syndrome that involves GIST, pulmonary chondroma, and extra-adrenal paraganglioma. The diagnosis of Carney’s triad requires the presence of at least two of these three components. Most patients have two tumors on presentation, with the most frequent combination being GIST and pulmonary chondroma. This form of the disease is named ‘‘incomplete Carney triad.’’ Carney triad is generally accepted to be a genetic disorder, but not